Junctional epidermolysis bullosa: a case report.
نویسندگان
چکیده
Epidermolysis bullosa (EB) is a group of genetically determined disorders characterized by blistering of the skin and mucosae. There are three major forms--simple, junctional and dystrophic--and each has several varieties. The present case report describes a male child with junctional EB. The aim of the report is to present the dietary situation and the dental status of the child, examples of potential dental and nutritional consequences, and the therapeutic interventions possible for children with this disease.
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ورودعنوان ژورنال:
- International journal of paediatric dentistry
دوره 15 2 شماره
صفحات -
تاریخ انتشار 2005